UMEM Educational Pearls

Title: Crowned dens syndrome

Category: Misc

Keywords: Neck pain, crowned dens syndrome (PubMed Search)

Posted: 12/22/2024 by Robert Flint, MD (Updated: 12/26/2024)
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Crowned dens syndrome is an acute inflammatory disease caused by deposition of calcium pyrophosphate dihydrate crystals or hydroxyapatite crystals in the soft tissue  and ligaments surrounding the dense. Patient presentation is severe pain in the neck and base of the skull, low grade fever,  and elevated inflammatory markers. It is most commonly seen in elderly females. Ct scan is the gold standard for diagnosis. Once meningitis and other significant infectious process has been excluded, treatment is anti inflammatory medications including steroids. 

 

References

  1. Gaillard F, Yap J, Yu Jin T, et al. Crowned dens syndrome. Reference article, Radiopaedia.org (Accessed on 22 Dec 2024) https://doi.org/10.53347/rID-42981
  2. Eggum,  et al.  A diagnosis fit for a queen: crowned dens syndrome. Clinical practice and cases in emergency medicine. November 2024. Volume 8, Number  4. P381.